Евразийские рекомендации по диагностике и лечению легочной гипертензии, ассоциированной с врожденными пороками сердца у взрослых (2021)

Автор: Чазова И.Е., Горбачевский С.В., Мартынюк Т.В., Шмальц А.А., Валиева З.С., Барышникова И.Ю., Глушко Л.А., Грамович В.В., Азизов В.А., Веселова Т.Н., Данилов Н.М., Зелвеян П.А., Иванов С.Н., Лазарева И.В., Матчин Ю.Г., Мукаров М.А., Наконечников С.Н., Сарыбаев А.Ш., Стукалова О.В., Шалаев С.В.

Журнал: Евразийский кардиологический журнал @eurasian-cardiology-journal

Рубрика: Клинические рекомендации

Статья в выпуске: 2, 2022 года.

Бесплатный доступ

Рекомендации ЕАК отражают точку зрения ЕАК и были подготовлены после тщательного изучения научных и медицинских данных, имеющихся на момент их публикации. ЕАК не несут ответственности в случае какого-либо противоречия, несоответствия и / или неоднозначности между Рекомендациями ЕАК и любыми другими официальными рекомендациями или руководствами, выпущенными соответствующими органами общественного здравоохранения, в частности, в отношении правильного использования медицинских или терапевтических стратегий. Медицинским работникам рекомендуется в полной мере учитывать Рекомендации ЕАК при оценке своего клинического суждения, а также при определении и реализации профилактических, диагностических или терапевтических медицинских стратегий. Тем не менее, Рекомендации ЕАК никоим образом не отменяют индивидуальную ответственность медицинских работников за принятие надлежащих и точных решений с учетом состояния здоровья каждого пациента и в консультации с этим пациентом и, при необходимости и/или необходимости, опекуна пациента. Рекомендации ЕАК не освобождают медицинских работников от полного и тщательного рассмотрения соответствующих официальных обновленных рекомендаций или руководств, выпущенных компетентными органами общественного здравоохранения, для рассмотрения каждого медицинского случая в свете современных научно обоснованных рекомендаций в соответствии с их этическими и профессиональными обязательствами. Кроме того, медицинский работник обязан проверять действующие правила и положения, касающиеся лекарств и медицинских изделий, на момент назначения по рецепту.

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Легочная гипертензия, легочная артериальная гипертензия, врожденный порок сердца, легочно-сосудистая болезнь, хирургическое лечение, атриосептостомия, специфическая терапия, клинические рекомендации

Короткий адрес: https://sciup.org/143179151

IDR: 143179151   |   DOI: 10.38109/2225-1685-2022-2-6-70

Список литературы Евразийские рекомендации по диагностике и лечению легочной гипертензии, ассоциированной с врожденными пороками сердца у взрослых (2021)

  • Чазова И.Е., Мартынюк Т.В., Валиева З.С. и соавт. Евразийские клинические рекомендации по диагностике и лечению легочной гипертензии. Евразийский кардиологический журнал. 2020; 1:78-122 [Chazova I.E., Martynyuk T.V., Valieva Z.S., et al). EURASIAN CLINICAL GUIDELINES ON DIAGNOSIS AND TREATMENT OF PULMONARY HYPERTENSION. Eurasian heart journal. 2020;(1):78-122. (In Russ.)] https://doi.org/10.38109/2225-1685-2020-1-78-122
  • Baumgartner H, De Backer J., Babu-Naraya S.V., et al. 2020 ESC Guidelines for the management of adult congenital heart disease: The Task Force for the management of adult congenital heart disease of the European Society of Cardiology (ESC). Endorsed by: Association for European Paediatric and Congenital Cardiology (AEPC), International Society for Adult Congenital Heart Disease (ISACHD). Eur Heart J. 2021; Vol. 42 (6): 563-645. https// doi.org/10.1093/eurheartj/ehaa554
  • Frost A., Badesch D., Simon J.R., et al. Diagnosis of pulmonary hypertension. Eur Respir J. 2019; 53: 1801904. https://doi.org/10.1183/13993003.01904-2018
  • Galie N., Humbert M., Vachiery J.L., et al. 2015 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension: The Joint Task Force for the Diagnosis and Treatment of Pulmonary Hypertension of the European Society of Cardiology (ESC) and the European Respiratory Society (ERS): Endorsed by: Association for European Paediatric and Congenital Cardiology (AEPC), International Society for Heart and Lung Transplantation (ISHLT). Eur. Heart J. 2016; 37: 67-119. https://doi.org/10.1183/13993003.01032-2015
  • Мартынюк Т.В. Легочная гипертензия: диагностика и лечение. Сер. Библиотека ФГБУ «НМИЦ кардиологии» Минздрава России. М.: ООО «Медицинское информационное агентство», 2018. 304 с. [Martynyuk T.V. Pulmonary hypertension: diagnosis and treatment. Moscow: LLC «Medical Information Agency», 2018:304 р. (In Russ.)]
  • Чазова И.Е., Архипова О.А., Мартынюк Т.В. Легочная артериальная гипертензия в России: анализ шестилетнего наблюдения по данным Национального регистра. Терапевтический архив. 2019; 91(1):24-32. [Chazova I.E., Arkhipova O.A., Martynyuk T.V. Pulmonary arterial hypertension in Russia: six-year observation analysis of the National Registry// Terapevticheskii arkhiv. 2019; Vol. 91 (1):25-31. (In Russ.)] https:// doi.org/10.26442J00403660.2019.01.000024
  • Dimopoulos K., Wort S.J., Gatzoulis M.A. Pulmonary hypertension related to congenital heart disease: A call for action. Eur Heart J. 2014; 35:691-700. https://doi.org/10.1093/eurbeartj/eht437
  • Lowe B.S., Therrien J., Ionescu-Ittu R., et al. Diagnosis of pulmonary hypertension in the congenital heart disease adult population: impact on outcomes. J Am Coll Cardiol. 2011; 58: 538-46. https://doi.org/10.1016/j. jacc.2011.03.033
  • Легочная гипертензия, в том числе хроническая тромбоэмболическая легочная гипертензия. Российские клинические рекомендации, 2020 [Pulmonary hypertension, including chronic thromboembolic pulmonary hypertension. Russian clinical guidelines, 2020 (In Russ.)] http:// cr.rosminzdrav.ru№!/recomend/137
  • Kovacs G., Berghold A., Scheidl S., et al. Pulmonary arterial pressure during rest and exercise in healthy subjects: a systematic review. Eur Respir J. 2009; 34 (4): 888-94. https://doi.org/10.1183/09031936.00145608
  • Kaemmerer H., Apitz C., Brockmeier K., et al. Pulmonary hypertension in adults with congenital heart disease: Updated recommendations from the Cologne Consensus Conference 2018. Int J of Cardiology. 2018; 272:79-88. https://doi.org/10.1016/j.ijcard.2018.08.078
  • Горбачевский С.В., Шмальц А.А. Диагностика легочной гипертензии, ассоциированной с врожденными пороками сердца. Часть 1. Определение, классификация и первичное обследование пациентов. Российский вестник перинатологии и педиатрии. 2021; 66 (5):28-37 [Gorbachevsky S.V., Shmalts A.A. Diagnosis of pulmonary hypertension associated with congenital heart disease. Part 1. Definition, classification and initial examination of patients. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2021;66(5):28-37. (In Russ.)] https://doi.org/10.21508/1027-4065-2021-66-5-28-37
  • Rosenzweig E.B., Abman S.H., Adatia I., et al. Paediatric pulmonary arterial hypertension: updates on definition, classification, diagnostics and management. Eur Respir J. 2019; 53(1). https://doi. org/10.1183/13993003.01916-2018
  • Simonneau G., Gatzoulis M.A., Adatia I., et al. Updated clinical classification of pulmonary hypertension. J Am Coll Cardiol. 2013; 62 (25 Suppl): D34-41. httpsJ/doi.orgJ10.1016/\.\acc.2013.10.029
  • Cantor W.J., Harrison D.A., Moussadji J.S., et al. Determinants of survival and length of survival in adults with Eisenmenger syndrome, Am J. Cardiol. 1999; 84: 677-81. httpsJ/doi.org/10.1016/S0002-9149(99)00415-4
  • Galie N., Hoeper M.M., Humbert M., et al. Guidelines for the diagnosis and treatment of pulmonary hypertension: The Task Force for the Diagnosis and Treatment of Pulmonary Hypertension of the European Society of Cardiology (ESC) and the European Respiratory Society (ERS), endorsed by the International Society of Heart and Lung Transplantation (ISHLT). Eur Heart J. 2009; 30:2493-537. https://doi.org/10.1093/eurheartj/ehp297
  • Stout K.K., Daniels C.J., Aboulhosn J.A., et al. 2018 AHA/ACC Guideline for the Management of Adults With Congenital Heart Disease: A Report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines. Circulation. 2019; 139: e698-e800. https://doi. org/10.1161/CIR.0000000000000603
  • Бокерия Л.А., Горбачевский С.В., Шмальц А.А., соавт. Гемодинамическая коррекция функционально единственного желудочка сердца после ранее выполненного суживания легочной артерии. Грудная и сердечно-сосудистая хирургия. 2008; 5:27-34. [Bockeria L.A., Gorbacheusky S.V., Shmalts A.A., et al. Hemodinamic correction of the single functional ventricle after prior pulmonary arterial narrowing. Russian Journal of Thoracic and Cardiovascular Surgery. 2008; 5:27-34 (In Russ.)]
  • Бокерия Л.А., Горбачевский С.В., Шмальц А.А. Легочная артериальная гипертензия, ассоциированная с врожденными пороками сердца у взрослых (клиническая рекомендация). Грудная и сердечно-сосудистая хирургия. 2017; 59 (2): 135-47. [Bockeria L.A., Gobachevskiy S.V., Shmal's A.A. Pulmonary arterial hypertension associated with congenital heart disease in adults (clinical guidelines). Grudnaya i Serdechno-Sosudistaya Khirurgiya, Thoracic and Cardiovascular Diseases, Russian journal). Grudnaya i serdechno-sosudistaya khirurgiya (Russian Journal of Thoracic and Cardiovascular Surgery).2017; 59(2):135-147. (In Russ)]. https://doi. org/10.24022/0236-2791-2017-59-2-135-147
  • Легочная гипертензия у детей. Российские клинические рекомендации, 2017. [Pulmonary hypertension in children. Russian clinical guidelines, 2017 (In Russ)]. http//cr.rosminzdrav.ru/#!/recomend/901
  • Гипертензионная сосудистая болезнь легких, ассоциированная с врожденными пороками сердца, у детей. Российские клинические рекомендации, 2018. [Hypertensive pulmonary vascular disease associated with congenital heart disease in children. Russian clinical guidelines, 2018 (In Russ)]. httpJ/cr.rosminzdrav.ru/#!/schema/356
  • Cerro M.J., Abman S., Diaz G., et al. A consensus approach to the classification of pediatric pulmonary hypertensive vascular disease: Report from the PVRI Pediatric Taskforce, Panama 2011. Pulm Circ. 2011; 1(2):286-98. https://doi.org/10.4103/2045-8932.83456
  • Чазова И.Е., Мартынюк Т.В. Легочная гипертензия. Москва. Практика. 2015, 928 с. [Chazova I.E., Martynyuk T.V. Pulmonary hypertension. Moscow. Practice. 2015, 928 p. (In Russ.)]
  • Apitz C., Hansmann G., Schranz D. Hemodynamic assessment and acute pulmonary vasoreactivity testing in the evaluation of children with pulmonary vascular disease. Expert consensus statement on the diagnosis and treatment of paediatric pulmonary hypertension. The European Paediatric Pulmonary Vascular Disease Network, endorsed by ISHLT and DGPK. Heart. 2016; 102 (Suppl 2): ii23-9. http://dx.doi.org/10.1136/heartjnl-2014-307340
  • Moceri P., Kempny A., Liodakis E., et al. Physiological differences between various types of Eisenmenger syndrome and relation to outcome. Int J Cardiol. 2015; 179:455-460. https://doi.org/10.1016/j.ijcard.2014.11.100
  • Kozlik-Feldmann G., Hansmann, D., et al. Pulmonary hypertension in children with congenital heart disease (PAH-CHD, PPHVD-CHD). Expert consensus statement on the diagnosis and treatment of paediatric pulmonary hypertension. The European Paediatric Pulmonary Vascular Disease Network, endorsed by ISHLT and DGPK, Heart 2016; 102 (Suppl 2): i42-ii8. http://dx.doi.org/10.1136/heartjnl-2015-308378
  • van der Linde D., Konings E.E., Slager M.A., et al. Birth prevalence of congenital heart disease worldwide: a systematic review and meta-analysis. J Am Coll Cardiol 2011; 58: 2241-47. https//doi.org/10.1016/j. jacc.2011.08.025
  • Liu Y., Chen S., Zuhlke L, et al. Global birth prevalence of congenital heart defects 1970-2017: updated systematic review and meta-analysis of 260 studies. Int J Epidemiol. 2019; 48:455-46. https://doi.org/10.1093/ije/dyz009
  • Lytzen R., Vejlstrup N., Bjerre J., et al. Live-born major congenital heart disease in Denmark: incidence, detection rate, and termination of pregnancy rate from 1996 to 2013. JAMA Cardiol 2018; 3: 829-37. https//doi. org/10.1001/jamacardio.2018.2009
  • Moons P., Bovijn L., Budts W., et al. Temporal trends in survival to adulthood among patients born with congenital heart disease from 1970 to 1992 in Belgium. Circulation. 2010; 122: 2264-72. https://doi.org/10.1161/ CIRCULATI0NAHA.110.946343
  • MarelliA.J., Ionescu-Ittu R., MackieA.S., et al. Lifetime prevalence of congenital heart disease in the general population from 2000 to 2010. Circulation. 2014; 130: 749-56. https://doi.org/10.1161/CIRCULATI0NAHA.113.008396
  • Van de Bruaene A., Delcroix M., Pasquet A., et al. The Belgian Eisenmenger syndrome registry: Implications for treatment strategies? Acta Cardiol. 2009;64:447-53. https//doi.org/10.2143/AC.64.4.2041608
  • van Riel A.C., Schuuring M.J., van Hessen I.D., et al. Contemporary prevalence of pulmonary arterial hypertension in adult congenital heart disease following the updated clinical classification. Int J Cardiol. 2014; 174: 299-305. https//doi.org/10.1016/j.ijcard.2014.04.072
  • Manes A., Palazzini M., Leci E., et al. Current era survival of patients with pulmonary arterial hypertension associated with congenital heart disease: a comparison between clinical subgroups. Eur Heart J. 2014; 35: 716-24. https://doi.org/10.1093/eurheartj/eht072
  • McLaughlin V.V., Presberg K.W., Doyle R.L., et al. Prognosis of pulmonary arterial hypertension: ACCP evidence-based clinical practice guidelines. Chest. 2004. 126 (1 Suppl):78S-92S. https://doi.org/10.1378/chest.126.1_ suppl.78S
  • Marelli A.J., Mackie A.S., Ionescu-Ittu R., et al. Congenital heart disease in the general population: Changing prevalence and age distribution. Circulation. 2007; 115:163-72. https//doi.org/10.1161/CIRCULATI0NAHA.106.627224
  • Duffels M.G., Engelfriet P.M., Berger R.M. et al. Pulmonary arterial hypertension in congenital heart disease: an epidemiologic perspective from a Dutch registry. Int J Cardiol. 2007; 120(2):198-204. https//doi. org/10.1016/j.ijcard.2006.09.017
  • Ramjug S., Hussain N., Hurdman J. et al. Pulmonary arterial hypertension associated with congenital heart disease: Comparison of clinical and anatomic-pathophysiologic classification. J Heart Lung Transplant. 2016. 35(5):610-18. https//doi.org/10.1016/j.healun.2015.12.016
  • Diller G.P, Dimopoulos K., Kafka H., et al. Model of chronic adaptation: Right ventricular function in Eisenmenger syndrome. Eur. Heart J. Suppl. 2007; 9:H54-H60. https://doi.org/10.1093/eurheartj/sum019
  • Alonso-Gonzalez R., Lopez-Guarch C.J., Subirana-Domenech M.T., et al. Pulmonary hypertension and congenital heart disease: An insight from the REHAP National Registry. Int J Cardiol. 2015; 184:717-23. https//doi. org/10.1016/j.ijcard.2015.02.031
  • Kempny A., Hjortsh0j C.S., Gu H., et al. Predictors of Death in Contemporary Adult Patients With Eisenmenger Syndrome: A Multicenter Study. Circulation. 2017;135(15):1432-1440. https://doi.org/10.1161/ CIRCULATI0NAHA.116.023033
  • Morse J.H., Barst R.J., Fotino M. Familial pulmonary hypertension: immunogenetic findings in four Caucasian kindreds. Am Rev Respir Dis. 1992; 145:787-92. https://doi.org/10.1164/ajrccm/145.4_Pt_1.787
  • Roberts K.E., McElroy J.J., Wong W.P, et. al. BMPR2 mutations in pulmonary arterial hypertension with congenital heart disease. Eur. Respir. J. 2004; 24:371-74. https://doi.org/10.1183/09031936.04.00018604
  • Бокерия Л.А., Горбачевский С.В., Шмальц А.А. Легочная артериальная гипертензия, ассоциированная с врожденными пороками сердца у взрослых. Методическое пособие. НЦССХ им. А. Н. Бакулева РАМН, 2016. 28 с. ISBN 978-5-7982-0368-0. [Bockeria L.A., Gorbachevskiy S.V., Shmal's A.A. Pulmonary arterial hypertension associated with congenital heart disease in adults. Methodological manual. Bakoulev SCCS RAMS. 2016. 28 p. ISBN 978-5-7982-0368-0 (In Russ.)]
  • Хугаев Г.А., Шмальц А.А. Морфологическая оценка сосудов легких при легочной гипертензии, обусловленной врожденными пороками сердца. Архив патологии. 2021; 83 (5): 49-57. [Khugaev GA, Shmalts AA. Morphological assessment of pulmonary vessels in pulmonary arterial hypertension associated with congenital heart disease. Arkhiv Patologii. 2021;83(5):49-57. (In Russ.)] https://doi.org/10.17116/ patol20218305149
  • Rabinovitch M. Molecular pathogenesis of pulmonary arterial hypertension. J Clin Invest. 2012; 122 (12):4306-13. https://doi.org/10.1172/JCI60658
  • Iacobazzi D., Suleiman M.S., Ghorbel M., et al. Cellular and molecular basis of RV hypertrophy in congenital heart disease. Heart. 2016; 102(1):12-7. https://doi.org/10.1136/heartjnl-2015-308348
  • Bradford R., Tulloh R. Diagnosis and management of pulmonary hypertension in adult congenital heart disease. Br J Cardiac Nurs. 2008; 3:138-45.
  • Rubens C., Ewert R., Halank M., et al. Big endothelin-1 and endothelin-1 plasma levels are correlated with the severity of primary pulmonary hypertension. Chest. 2001. 120(5):1562-69. https://doi.org/10.1378/ chest.120.5.1562
  • Gorbachevsky Sv., Shmalts A.A. What can cause pulmonary vascular disease in functionally single ventricle? Anatomy & Physiology: Current Research. 2016; 6 (1). https://doi.org/10.4172/2161-0940.1000e137
  • Adatia I., Kothari S.S., Feinstein J.A. Pulmonary hypertension associated with congenital heart disease: pulmonary vascular disease: the global perspective. Chest 2010; 137(6):52-61. https://doi.org/10.1378/chest.09-2861
  • Шарыкин А.С. Врожденные пороки сердца. Руководство педиатров, кардиологов, неонатологов. -М.:Теремок.-2005.- 381 c. ISBN 5-97110011-4. [Sharykin A.S. Congenital heart disease. Guidelines for pediatricians, cardiologists, neonatologists. Moscow: Teremok. 2005:381. (In Russ.)]
  • Favoccia C., Constantine A.H., Wort S.J., et al. Eisenmengersyndrome and other types of pulmonary arterial hypertension related to adult congenital heart disease. Expert Review of Cardiovasc Therapy 2019; 17:449-59. https://doi.org/10.1080/14779072.2019.1623024
  • Baumgartner H., Bonhoeffer P., De Groot N.M., et al. ESC Guidelines for the management of grown-up congenital heart disease (new version 2010). European Paediatric Cardiology (AEPC), ESC Committee for Practice Guidelines (CPG). Eur Heart J. 2010; 31(23):2915-57. https://doi. org/10.1093/eurheartj/ehq249
  • Heath D., Edwards J.E. The pathology of hypertensive pulmonary vascular disease; a description of six grades of structural changes in the pulmonary arteries with special reference to congenital cardiac septal defects. Circulation. 1958; 4 (Part 1):533-47. https//doi.org/10.1161/01.CIR.18.4.533
  • Yamaki S., Horiuchi T., Miura M., et al. Pulmonary vascular disease in secundum atrial septal defect with pulmonary hypertension. Chest. 1986; 89(5):694-8. https//doi.org/10.1378/chest.89.5.694
  • Heath D., Helmholz H.F. Jr, Burchell H., et al. Relation between structural change in the small pulmonary arteries and the immediate reversibility of pulmonary hypertension following closure of ventricular and atrial septal defects. Circulation. 1958; 18(6):1167-74. https://doi.org/10.1161/01. cir.18.6.1167
  • Есипова И.К. Некоторые вопросы патологии лёгких. АН СССР. 1962. [Esipova I.K. Some questions in pulmonary pathology. The Academy of Sciences of the Soviet Union. 1962. (In Russ.)]
  • Haworth S.G., Rabinovitch M. Pulmonary circulation. In: Anderson RH, Baker EJ, Penny DJ, Redington AN, Rigby ML, Wernovsky G (eds). Paediatric Cardiology, 3rd edn. Churchill Livingstone, Elsevier, Philadelphia, PA, 2010:117-141.
  • Rabinovitch M., Haworth S.G., Castaneda A.R., et al. Lung biopsy in congenital heart disease: a morphometric approach to pulmonary vascular disease. Circulation. 1978; 58(6)1107-22. https://doi.org/10.1161/01. CIR.58.6.1107
  • Endo M., Yamaki S., Ohmi M., Tabayashi K. Pulmonary vascular changes induced by congenital obstruction of pulmonary venous return. Ann Thorac Surg. 2000; 69 (1):193-7. https//doi.org/10.1016/S0003-4975(99)01079-6
  • Dimopoulos K., Diller G.P., Opotowsky A.R., et al. Definition and Management of Segmental Pulmonary Hypertension. J Am Heart Assoc. 2018;7 (14):e008587. https://doi.org/10.1161/JAHA.118.008587
  • Thiene G., Frescura C., Bini R.M., et al. Histology of pulmonary arterial supply in pulmonary atresia with ventricular septal defect. Circulation. 1979; 60 (5):1066-74. https://doi.org/10.1161/01.cir.60.5.1066
  • Van Dissel A.C., Mulder B.J., Bouma B.J. The Changing Landscape of Pulmonary Arterial Hypertension in the Adult with Congenital Heart Disease. J of Clin Med. 2017; 6(4):40. https://doi.org/10.3390/jcm6040040
  • Горбачевский С.В., Шмальц A.A., Плотникова Л.Р. Легочная гипертензия у детей с врожденными пороками сердца. Москва. 2018. [Gorbachevsky S.V., Shmalts A.A., Plotnikova L.R. Pulmonary hypertension in children with congenital heart disease. Moscow; OOO «Kedr», 2018; 91. (in Russ.)]
  • Бокерия ЛА, Горбачевский С.В., Школьникова МЛ. Легочная гипертензия у детей. Москва. Дктелион фармасьютикалз; 2013. [Pulmonary hypertension in children. Editors L.A. Bockeria, S.V. Gorbachevsky, M.A. Shkolnikova. Moscow: Aktelion farmas'yutikalz, 2013; 416. (in Russ.)]
  • Горбачевский С.В., Шмальц A.A. Гипертензионная сосудистая болезнь легких, ассоциированная с врожденными пороками сердца. В кн.: Бокерия ЛА, Шаталов К.В. Детская кардиохирургия. Руководство для врачей. Москва: НЦССХ им. A.H. Бакулева; 2016:833-50. [Gorbachevsky S.V., Shmalts A.A. Hypertensive pulmonary vascular disease associated with congenital heart defects. In: L.A. Bockeria, K.V. Shatalov (eds.). Pediatric cardiac surgery. A guide for doctors. Moscow, 2016; 833-850. (in Russ.)]
  • Hansmann G., Koestenberger M., Alastalo T.P., et al. 2019 updated consensus statement on the diagnosis and treatment of pediatric pulmonary hypertension: The European Pediatric Pulmonary Vascular Disease Network (EPPVDN), endorsed by AEPC, ESPR and ISHLT. J Heart Lung Transplant. 2019; 38(9):879-901. https://doi.org/10.1016/j. healun.2019.06.022
  • Lammers A.E., Apitz C., Zariner P., et al. Diagnostics, monitoring and outpatient care in children with suspected pulmonary hypertension/paediatric pulmonary hypertensive vascular disease. Expert consensus statement on the diagnosis and treatment of paediatric pulmonary hypertension. The European Paediatric Pulmonary Vascular Disease Network, endorsed by ISHLTand DGPK. Heart. 2016; 102 (Suppl 2):ii1-13. https://doi.org/10.1136/ heartjnl-2015-307792
  • Dimopoulos K., Diller G.P Pulmonary Hypertension in Adult Congenital Heart Disease. Springer; 2017. 368p. https://doi.org/10.1007/978-3-319-46028-4
  • Dimopoulos K., Prapa M., Gatzoulis M. Eisenmenger syndrome and other types of pulmonary arterial hypertension related to congenital heart disease. In: Pediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care. Springer; 2013. https://doi.org/10.1007/978-1-4471-4619-3_182
  • Ikegami R., Ozaki K., Ozawa T., et al. Percutaneous Coronary Intervention for a Patient with Left Main Coronary Compression Syndrome. Intern Med. 2018; 57 (10):1421-4. https://doi.org/10.2169/internalmedicine.9534-17
  • Butera G., Mansour N.B., De Marco F. Emergency transcatheter coronary intervention for left main compression secondary to pulmonary hypertension in a 4-year-old child. Catheter Cardiovasc Interv. 2019; 93(1):105-7. https:// doi.org/10.1002/ccd.27796
  • Mamas M.A., Clarke B., Mahadevan V.S. Embolisation of systemic-to-pulmonary collaterals in patients with the Eisenmenger reaction presenting with haemoptysis. Cardiol Young. 2008; 18 (5):528-31. https://doi. org/10.1017/S1047951108002680
  • Larici A.R., Franchi P., Occhipinti M., et al. Diagnosis and management of hemoptysis. Diagn Interv Radiol. 2014; 20 (4):299-309. https://doi. org/10.5152/dir. 2014.13426
  • Broberg C.S., Ujita M., Prasad S. et al. Pulmonary arterial thrombosis in Eisenmenger syndrome is associated with biventricular dysfunction and decreased pulmonary flow velocity. J Am Coll Cardiol. 2007; 50(7):634-42. httpsJ/doi.org/10.1016/j.jacc.2007.04.056
  • Placik B., Rodbard S., McMahon J., Swaroop S. Pulmonary artery dissection and rupture in Eisenmenger's syndrome. Vasc Surg. 1976; 10(2):72-80. https://doi.org/10.1177/153857447601000203
  • Areco D., Pizzano N. Pulmonary artery dissection: echocardiographic findings and diagnosis. Echocardiography. 2003; 20 (4): 375-7. httpsJ/doi. org/10.1046/j.1540-8175.2003.03044.x
  • Mikhail G.W., Gibbs J.S., Yacoub M.H. Pulmonary and systemic arterial pressure changes during syncope in primary pulmonary hypertension. Circulation. 2001; 104(11):1326-7. https://doi.org/10.1161/ hc3601.095274
  • Moledina S., Hislop A.A., Foster H., et al. Childhood idiopathic pulmonary arterial hypertension: a national cohort study. Heart. 2010; 96(17):1401-6. https://doi.org/10.1136/hrt.2009.182378
  • Чазова И. E., Aвдеев С. H., Царева H.A., соавт. Клинические рекомендации по диагностике и лечению легочной гипертонии. Терапевтический архив. 2014; 9:4-23. [Chazova I.E., Avdeev S.N., Tsareva N.A., et al. Clinical guidelines for the diagnosis and treatment of pulmonary hypertension. Terapevticheskii arkhiv. 2014; 9:4-23. (In Russ.)]
  • Kaemmerrer H., Koichiro N., Oechslin E., et al. Pulmonary Arterial Hypertension in Congenital Heart Disease: Eisenmenger's Syndrome - A Global Perspectiv. 1st edition. Bremen: UNI-MED; 2013.
  • Oechslin E., Mebus S., Schulze-Neick I., et al. The Adult Patient with Eisenmenger Syndrome: A Medical Update after Dana Point Part III: Specific Management and Surgical Aspects. Cur Cardiol Rev. 2010; 6 (4):363-72. https://doi.org/10.2174/157340310793566127
  • Labombarda F., Kerros H., Grollier G. Eisenmenger syndrome due to a large ductus arteriosus. Arch Cardiovasc Dis. 2010; 103 (11-12):623-5. https://doi. org/10.1016/j.acvd.2010.02.004
  • Dimopoulos K. Eisenmenger syndrome in an adult patient with a large patent ductus arteriosus. Eur Respir Rev. 2013; 22(130): 558-64. https//doi. org/10.1183/09059180.00007013
  • Рябыкина Г.В., Блинова E.B., Сахнова T.A. Электровекторкардиографическая диагностика гипертрофии правого желудочка у больных легочной гипертензией. Медицинский алфавит 2017; 8:3-17. [Ryabykina G.V., Blinova E.V., Sakhnova T.A. Electrovectorcardiographic diagnosis of right ventricular hypertrophy in patients with pulmonary hypertension. Practitioners' manual. Medical alphabet. 2017;1(8):52-66. (In Russ.)]
  • Kamphuis V.P., Haeck M.L., Wagner G.S., et al. Electrocardiographic detection of right ventricular pressure overload in patients with suspected pulmonary hypertension. J Electrocardiol. 2014; 47(2):175-82. https://doi. org/10.1016/j.jelectrocard.2013.10.010
  • Tongers J., Schwerdtfeger B., Klein G., et al. Incidence and clinical relevance of supraventricular tachyarrhythmias in pulmonary hypertension. Am Heart J. 2007; 153:127-32. https//doi.org/10.1016/j.ahj.2006.09.008
  • Юрпольская ЛЛ, Шмальц A.A. Рентгенография, рентгеновская компьютерная и магнитно-резонансная томография при легочной гипертензии, ассоциированной с врожденными пороками сердца. Детские болезни сердца и сосудов. 2021; 18(2):83-93. [Yurpol'skaya L.A., Shmalts A.A. X-ray methods and magnetic resonance imaging in pulmonary hypertension associated with congenital heart disease. Children's Heart and Vascular Diseases. 2021;18 (2):83-93 (in Russ.)] https://doi. org/10.24022/1810- 0686-2021-18-2-83-93
  • Цаллагова З.С., Лазуткина В.К. Возможности традиционной рентгенографии в оценке легочной артериальной гипертензии. Медицинская визуализация. 2001; 4:59-63. [Tsallagova Z.S., Lazutkina V.K. Possibilities of radiography in assessment of pulmonary arterial hypertension. Meditsinskaya vizualizatsiya. 2001; (4):58-63. (In Russ.)]
  • Рентгенодиагностика заболеваний сердца и сосудов. /Ред. M.A. Иваницкая. - М., «Медицина», 1970. [X-ray diagnostics of diseases of the heart and blood vessels. /Ed. M.A. Ivanitskaya. - M., "Medicine", 1970. (In Russ)].
  • Рентгенодиагностика в педиатрии. Руководство для врачей в 2-х томах. /Под ред. В.Ф.Баклановой, М.АФилиппкина. - М.: Медицина,-1988.- Т.1.- 448 P. [X-ray diagnostics in pediatrics. Guide for doctors in 2 volumes. / Ed. V.F.Baklanova, M.A.Filippkina.- M.: Medicine, -1988.-V.1.- 448 P. (In Russ)].
  • Детская кардиология. Под ред. Дж.Хоффмана. Пер.с англ. - М.: Практика.- 2006.-543С. [Pediatric cardiology. Ed. J. Hoffman. Translation from English - M .: Practice. - 2006.-543P. (In Russ.)]
  • Коробкова И.З., Лазуткина В.К., Низовцова ЛЛ. и др. Методические аспекты рентгенологической оценки легочной гипертензии. Вестник рентгенологии и радиологии. 2015. 4: 45-53 [Korobkova I.K., Lazutkina V.K., Nizovtsova L.A., Riden T.V. Radiographic assessment of pulmonary hypertension: Methodical aspects. Journal of radiology and nuclear medicine. 2015;(4):46-53. (In Russ.)] https://doi.org/10.20862/0042-4676-2015-0-4-14-21
  • Dimopoulos K., Giannakoulas G., Bendayan I., et al. Cardiothoracic ratio from postero-anterior chest radiographs: a simple, reproducible and independent marker of disease severity and outcome in adults with congenital heart disease. Int J Cardiol. 2013.166:453-7. https//doi.org/10.1016/j. ijcard.201110.125
  • Freedom R.M., Yoo Shi-joon, Mikailian H., Williams W.G. The Natural and Modified History of Congenital Heart Disease. 2008. Wiley-Blackwell- 904 p. httpsMoi.org/10.1002/9780470986905.ch1
  • Freedom R. M., Benson L.N., Smallhorn J.F. Neonatal Heart Disease. Springer-Verlag London 1992, 881p. https://doi.org/10.1007/978-1-4471-1814-5
  • Koestenberger M., Apitz C., Abdul-Khaliq H., Hansmann G. Transthoracic echocardiography for the evaluation of children and adolescents with suspected or confirmed pulmonary hypertension. Expert consensus statement on the diagnosis and treatment of paediatric pulmonary hypertension. The European Paediatric Pulmonary Vascular Disease Network, endorsed by ISHLT and D6PK. Heart. 2016; 102 (Suppl 2): ii14-22. https://doi.org/10.1136/heartjnl-2014-307200
  • Anderson R.H., Baker E.J., Penny D.J., et al. Paediatric cardiology. 3d edition. Elsevier, 2009.
  • Барышникова И.Ю., Шмальц А.А. Диагностика легочной гипертензии, ассоциированной с врожденными пороками сердца. Часть 2. Эхокардиография. Российский вестник перинатологии и педиатрии. 2021; 66 (6): 23-32. [Baryshnikova I.Yu., Shmalts A.A. Diagnosis of pulmonary hypertension associated with congenital heart disease. Part 2. Echocardiography. Russian Bulletin of Perinatology and Pediatrics. 2021; 66(6):23-32 (In Russ). https://doi.org/10.21508/1027-4065-2021-66-6-23-32
  • Li W., West C., McGhie J., et al. Consensus recommendations for echocardiography in adults with congenital heart defects from the International Society of Adult Congenital Heart Disease (ISACHD). Int J Cardiol. 2018; 272:77-83. https://doi.org/10.1016/lijcard.2018.07.058
  • Augustine D.X., Coates-Bradshaw L.D., Willis J., et al. BSE pulmonary hypertension guideline 2018; 5 (3): G11-G24. https://doi.org/10.1530/ERP-17-0071
  • Rudski LG., Lai W.W., Afi lalo J., et al. Guidelines for the Echocardiographic Assessment of the Right Heart in Adults: A Report from the American Society of Echocardiography Endorsed by the European Association of Echocardiography, a registered branch of the European Society of Cardiology, and the Canadian Society of Echocardiography. J Am Soc Echocardiogr. 2010; 23:685-713. https//doi.org/10.1016/j.echo.2010.05.010
  • Zaidi A., Knight D.S., Augustine D.X., et al. Echocardiographic assessment of the right heart in adults: a practical guideline from the British Society of Echocardiography. 2020; 7 (1): G19-G41. https://doi.org/10.1530/ERP-19-0051
  • Amsallem M., Sternbach J.M., Adigopula S., et al. Addressing the controversy of estimating pulmonary arterial pressure by echocardiography. J Am Soc Echocardiogr. 2016; 29:93-102. httpsJ/doi.org/10.1016/j.echo.2015.11.001
  • Fisher M.R., Forfia P.R., Chamera E., et al. Accuracy of Doppler echocardiography in the hemodynamic assessment of pulmonary hypertension. Am J Respir Crit Care Med. 2009; 179 (7): 615-21. https://doi. org/10.1164/rccm.200811-16910C
  • Rimington H., Chambers J.B. Echocardiography: a practical guide for reporting and interpretation. Third edition. CRC Press; 2016. https//doi. org/10.1201/b19334
  • Lang R.M., Badano L.P., Mor-Avi V., et al. Recommendations for Cardiac Chamber Quantification by Echocardiography in Adults: An Update from the American Society of Echocardiography and the European Association of Cardiovascular Imaging. J Am Society of Echocardiography. 2015; 28 (1): 1-39. https//doi.org/10.1016/j.echo.2014.10.003
  • Abraham S., Weismann C.G. Left ventricular end-systolic eccentricity index for assessment of pulmonary hypertension in infants. Echocardiography. 2016; 33:910-15. https://doi.org/10.1111/echo.13171
  • Nagueh S.F., Smiseth O.A., Appleton C.P., et al. Recommendations for the Evaluation of Left Ventricular Diastolic Function by Echocardiography: An Update from the American Society of Echocardiography and the European Association of Cardiovascular Imaging. J Am Soc Echocardiogr. 2016; 29:277-314. https://doi.org/10.1016/j.echo.2016.01.011
  • Friedberg M., Merten L. Tissue velocities, strain, and strain rate for echocardiographic assessment of ventricular function in congenital heart disease. European J Echocardiography. 2009; 10: 585-93. https//doi. org/10.1093/ejechocard/jep045
  • Lai W.W., Mertens L.L., Cohen M.S., Geva T. Echocardiography in pediatric and congenital heart disease. From Fetus to Adult. Second Edition. Wiley Blackwell; 2016.
  • Moceri P., Li W., Dimopoulos K. Echocardiography in the Diagnosis and Follow-Up of Patients with Pulmonary Arterial Hypertension Associated with Congenital Heart Disease. In: Dimopoulos K, Diller GP (eds). Pulmonary Hypertension in Adult Congenital Heart Disease. Springer; 2017. https://doi.org/10.1007/978-3-319-46028-4_11
  • Бокерия ЛА, Барышникова И.Ю., Горбачевский С.В. Эхокардиография в диагностике и оценке легочной гипертензии. Учебное пособие. Москва. 2017. [Bokeriya L.A., Baryshnikova I.Yu., Gorbachevsky S.V Echocardiography in the diagnosis and assessment of pulmonary hypertension. Tutorial. Moscow, 2017; 54 р. (In Russ.)]
  • Mertens L., Friedberg M.K. Systolic ventricular function. In: Echocardiography in Pediatric and Congenital Heart Disease: From Fetus to Adult; 2016, Hoboken, US: Wiley-Blackwell, p.96-131.
  • Gurudevan S.V., Malouf P.J., Kahn A.M., et al. Noninvasive assessment of pulmonary vascular resistance using Doppler tissue imaging of the tricuspid annulus. J Am Soc Echocardiogr. 2007; 20 (10):1167-71. https://doi.org/10.1016/j.echo.2007.02.004
  • Sutherland G.R., Di Salvo G., Claus P., et al. Strain and strain rate imaging: a new clinical approach to quantifying regional myocardial function. J Am Soc Echocardiogr 2004; 17: 788-802. https://doi. org/10.1016/j.echo.2004.03.027
  • D'Alto M., Dimopoulos K., Budts W., et al. Multimodality imaging in congenital heart disease-related pulmonary arterial hypertension. Heart. 2016; 102 (12): 910-18. https://doi.org/10.1136/heartjnl-2015-308903
  • Puchalski M.D., Lui G.K., Miller-Hance W., et al. Guidelines for Performing a Comprehensive Transesophageal Echocardiographic. Journal of the American Society of Echocardiography. 2019; 32 (2): 173-215. https:// doi.org/10.1016/j.echo.2018.08.016
  • Шария А.М., Мартынюк Т.В., Терновой С.К., Шария М.А. Возможности магнитно-резонансной томографии в диагностике легочной артериальной гипертензии. Кардиология. 2021;61(6):97-104. [Shariya A.M., Martynyuk T.V., Ternovoy S.K., Shariya M.A. Possibilities of Magnetic Resonance Tomography in Diagnosis of Pulmonary Arterial Hypertension. Kardiologiia. 2021;61(6):97-104. (In Russ.)] https://doi.org/10.18087/cardio.202l6.n1185
  • Бокерия Л.А., Макаренко В.Н., Юрпольская Л.А. Компьютерная и магнитно-резонансная томография в диагностическом алгоритме врожденных пороков сердца: Что? Когда? Кому?-"за" и "против". Грудная и сердечно-сосудистая хирургия 2014; 3: 4-13. [L.A. Bockeria, V.N. Makarenko, L.A. Yurpol'skaya. Computer tomography and magnetic resonance imaging in the diagnostic algorithm of congenital heart disease: what, when, who? - "fof and "against". Russian Journal of Thoracic and Cardiovascular Surgery. 2014; 3:4-13. (In Russ.)]
  • Latus H., Kuehne T., Beerbaum Ph., et all. Cardiac MR and CT imaging in children with suspected or confirmed pulmonary hypertension/ pulmonary hypertensive vascular disease. Expert consensus statement on the diagnosis and treatment of paediatric pulmonary hypertension. The European Paediatric Pulmonary Vascular Disease Network, endorsed by ISHLT and DGPK. Heart. 2016; 102: ii30-ii35. https://doi.org/10.1136/ heartjnl-2015-308246
  • van Wolferen S.A., Marcus J.T., Boonstra A., et al. Prognostic value of right ventricular mass, volume, and function in idiopathic pulmonary arterial hypertension. Eur Heart J. 2007. 28:1250-7. https://doi.org/10.1093/ eurheartj/ehl477
  • Belokon N.A., Podzolkov V.P., Mitrofanov I.O. Congenital heart disease.- M .: Medicine.-1990.- 352p. (In Russ).
  • Brignole M., Auricchio A., Baron-Esquivias G., et al. 2013 ESC Guidelines on cardiac pacing and cardiac resynchronization therapy: the Task Force on cardiac pacing and resynchronization therapy of the European Society of Cardiology (ESC). Developed in collaboration with the European Heart Rhythm Association (EHRA). Eur Heart J. 2013; 34: 2281-329. https//doi. org/10.1093/europace/eut206
  • Radenkovic D., Weingärtner S., Ricketts L., et al. T1 mapping in cardiac MRI. Heart Fail Rev. 2017; 22:415-430. https://doi.org/10.1007/s10741-017-9627-2
  • Salerno M., Sharif B., Arheden H., et al. Recent Advances in Cardiovascular Magnetic Resonance Techniques and Applications. Cir.cCardiovasc.Imaging. 2017; 10 :e003951. https://doi.org/10.1161/CIRCIMAGING.116.003951
  • European Medicines Agency. EMA's final opinion confirms restrictions on use of linear gadolinium agents in body scans. https:// httpsJ/www.ema.europa. eu/en/documents/press-release/emas-final-opinion-confirms-restrictions-use-linear-gadolinium-agents-body-scans_en.pdf
  • Odagiri K., Inui N., Hakamata A., et al. Noninvasive evaluation of pulmonary arterial blood flow and wall shear stress in pulmonary arterial hypertension with 3D phase contrast magnetic resonance imaging. Springer Plus 2016; 5: 1071. https://doi.org/10.1186/s40064-016-2755-7
  • Torbicki A. Cardiac magnetic resonance in pulmonary arterial hypertension: a step in the right direction. Eur Heart J 2007; 28: 1187-1189. https://doi. org/10.1093/eurheartj/ehm074
  • Perloff J.K., Marelli A. Perloffs Clinical Recognition of Congenital Heart Disease: Expert Consult Online and Print, 6e. 6th edition. Philadelphia: Saunders; 2012.
  • de Siqueira M.E.M.., Pozo E., Fernandes V.R., et all. Characterization and clinical significance of right ventricular mechanics in pulmonary hypertension evaluated with cardiovascular magnetic resonance feature tracking. J of CardiovascMagn Res- 2016; https://doi.org/10.1186/s12968-016-0258-x
  • Tello K., Dalmer A., Vanderpool R., et al. Cardiac Magnetic Resonance Imaging-Based Right Ventricular Strain Analysis for Assessment of Coupling and Diastolic Function in Pulmonary Hypertension. JACC Cardiovasc Imaging. 2019; 12 (1): 2155-64. https//doi.org/10.1016/j.jcmg.2018.12.032
  • Рентгенодиагностика заболеваний сердца и сосудов. Ред. М.А. Иваницкая. М., «Медицина», 1970. [X-ray diagnostics of diseases of the heart and blood vessels. Ed. M.A. Ivanitskaya. M., "Medicine", 1970 (In Russ)].
  • Макаренко В.Н., Юрпольская Л.А., Зеленикин М.М., Шинкарева Т.В. Компьютерная томография в оценке пациентов после операции Фонтена. Бюллетень НЦССХ им. А.Н.Бакулева РАМН. 2010; 11 (1): 46-50. [Makarenko V.N., Yurpolskaya L.A., Zelenikin M.M., Shinkareva T.V. Computed tomography in the evaluation of patients after Fontan surgery. Bulletin of the NCSSH them. A.N. Bakulev RAMS. 2010; 11(1)46-50. (In Russ)].
  • Kilner P., Nichol E., Rubens M. The roles of CT and CMR in Adult Congenital Heart Disease. In: ESC Textbook of Cardiovascular Imaging. 2nd ed, Oxford:Oxford University Press; 2015, p. 563-600.
  • Grosse-Wortmann L., Drolet Chr., Dragulescu An., et al. Aortopulmonary collateral flow volume affects early postoperative outcome after Fontan completion: A multimodality study. J. Thorac. Cardiovasc. Surg. 2012; 144:1329-36. https//doi.org/10.1016/j.jtcvs.2012.03.032
  • Habib G., Lancellotti P., Antunes M.J., et al. ESC Scientific Document Group. 2015 ESC Guidelines for the management of infective endocarditis: The Task Force for the Management of Infective Endocarditis of the European Society of Cardiology (ESC). Endorsed by: European Association for Cardio-Thoracic Surgery (EACTS), the European Association of Nuclear Medicine (EANM). Eur Heart J. 2015; 36:3075-3128. https://doi.org/10.1093/eurheartj/ ehv319
  • Ohno Y., Koyama H., Lee H.Y., Miura S.t all. Contrast-enhanced CT- and MRI-based perfusion assessment for pulmonary diseases: basics and clinical applications. Diagn Interv Radiol- 2016; 22: 407-421. https://doi. org/10.5152/dir.2016.16123
  • Pienn M., Kovacs G., Tscherner M., Avian A. et all. Non-invasive determination of pulmonary hypertension with dynamic contrast-enhanced computed tomography: a pilot study. Eur Radiol.-2014; 24:668-676. https:// doi.org/10.1007/s00330-013-3067-8
  • Соболев А.В., Шмальц А.А. Эндоваскулярная диагностика легочной гипертензии, ассоциированной с врожденными пороками сердца. Часть 1. Катетеризация сердца и ангиокардиография. Эндоваскулярная хирургия. 2021; 8 (3): 263-71. [SobolevA.V., Shmalts A.A. Endovascular diagnostics of pulmonary hypertension associated with congenital heart defects. Part 1. Cardiac catheterization and angiography. Russian journal of endovascular surgery. 2021; 8(3):263-71. (In Russ.)] https://doi.org/10.24183/2409-4080-2021-8-3-263-271
  • Guillinta P., Peterson K.L., Ben-Yehuda O. Cardiac catheterization techniques in pulmonary hypertension. Cardiol Clin. 2004; 22: 401-15. https://doi. org/10.1016/j.ccl.2004.04.011
  • Peterson K.L., Nicod P. Cardiac catheterization: methods, diagnosis, and therapy. Saunders, Philadelphia; 1997.
  • Barnett C., Ben-Yehuda О. Cardiac Catheterization in the Patient with Pulmonary Hypertension. Textbook of Pulmonary Vascular Disease Springer, Science+Business Media, LLC; 2011. https://doi.org/10.1007/978-0-387-87429-6
  • Горбачевский С.В., Белкина М.В., Колединский Д.Г., соавт. Инвазивный мониторинг давления в легочной артерии — объективный метод оценки степени тяжести легочной гипертензии у детей с врожденными пороками сердца. Детские болезни сердца и сосудов. 2006; 4: 77-81. [orbachevsky S.V., Belkina M.V., Koledinsky D.G., et al.
  • Invasive pulmonary artery pressure monitoring is an objective method for assessing the severity of pulmonary hypertension in children with congenital heart disease. Children's diseases of the heart and blood vessels. 2006; 4:77-81. (In Russ)].
  • Wilkinson J.L. The Fontan circulation. Results, late Follow-up and management. Heart Views. 2004; 4 (4): 73-78.
  • Fredenburg T.B., Johnson T.R., Cohen M.D. The Fontan Procedure:Anatomy, Complications, and Manifestations of Failure. RadioGraphics. 2011;31(2): 453-463. https://doi.org/10.1148/rg.312105027
  • Bergersen L., Foerster S., MarshallA.C., Meadows J. (eds). Congenital heart disease: the catheterization manual. Springer, New York; 2009. https//doi. org/10.1007/978-0-387-77292-9
  • Бокерия Л.А., Алекян Б.Г. (ред.). Руководство по рентгеноэндоваскулярной хирургии сердца и сосудов. Москва, НЦССХ им. А.Н. Бакулева РАМН; 2008.
  • Sitbon O., Humbert M., Jais X., et al. Long-term response to calcium channel blockers in idiopathic pulmonary arterial hypertension. Circulation. 2005; 111:3105-11. https://doi.org/10.1161/CIRCULATI0NAHA.104.488486
  • Barst R.J. Pharmacologically induced pulmonary vasodilatation in children and young adults with primary pulmonary hypertension. Chest. 1986; 89:497-503. https//doi.org/10.1378/chest.89.4.497
  • Rich S., Kaufmann E., Levy P.S. The effect of high doses of calcium-channel blockers on survival in primary pulmonary hypertension. N Engl J Med. 1992; 327:76-81. https://doi.org/10.1056/NEJM199207093270203
  • Douwes J.M., van Loon RLE, Hoendermis E.S, et al. Acute pulmonary vasodilator response in paediatric and adult pulmonary arterial hypertension: occurrence and prognostic value when comparing three response criteria. Eur Heart J. 2011; 32(24):3137-46. https://doi.org/10.1093/eurheartj/ehr282
  • Chessa M. Cardiac Catheterization. In: Dimopoulos K, Diller G.P. (eds). Pulmonary Hypertension in Adult Congenital Heart Disease. Springer; 2017.
  • Hoeper M.M., Lee S.H., Voswinckel R., et al. Complications of right heart catheterization procedures in patients with pulmonary hypertension in experienced centers. J Am Coll Cardiol. 2006; 48:2546-52. https://doi. org/10.1016/j.jacc.2006.07.061
  • Diller G.P., Dimopoulos K., Okonko D. et al. Exercise intolerance in adult congenital heart disease: Comparative severity, correlates, and prognostic implication. Circulation. 2005. 112:828-35. https://doi.org/10.1161/ CIRCULATIONAHA.104.529800.
  • Savarese G., Paolillo S., Costanzo P., et al. Do changes of 6-minute walk distance predict clinical events in patients with pulmonary arterial hypertension? А meta-analysis of 22 randomized trials. J Am Coll Cardiol 2012; 60:1192-1201. https//doi.org/10.1016/j.jacc.2012.01.083
  • Gabler N.B., French B., Strom B.L, et al. Validation of 6-minute walk distance as a surrogate end point in pulmonary arterial hypertension trials. Circulation 2012; 126:349-56. https//doi.org/10.1161/CIRCULATI0NAHA.112.105890
  • Глушко Л.А., Шмальц А.А. Оценка состояния кардиореспираторной системыi при легочной гипертензии, ассоциированной с врожденными пороками сердца. Креативная кардиология. 2021; 15 (2): 167-179. [Glushko L.A., Shmalts А.А. Assessment of the state of the cardiorespiratory system in pulmonary hypertension associated with congenital heart disease. Creative cardiology. 2021; 15(2): 167-179. (In Russ)].
  • Arena R., Lavie C.J., Milani R.V., et al. Cardiopulmonary exercise testing in patients with pulmonary arterial hypertension: an evidence-based review. J Heart Lung Transplant. 2010; 29 (2): 159-73. https//doi.org/10.1016/j. healun.2009.09.003
  • Johnson M.K., Thompson S. The role of exercise testing in the modern management of pulmonary arterial hypertension. Diseases. 2014; 2:120-47. https://doi.org/10.3390/diseases2020120
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